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Insufficient pancreatic exocrine function can cause steatorrhea and malabsorption due to a lack of digestive enzymes. The most common cause in children is cystic fibrosis. Treatment involves pancreatic enzyme replacement therapy using microsphere formulations that are protected from stomach acid. High doses of enzymes are needed for full digestion and absorption. Adjuvant therapies also aim to optimize acid-base balance and bile acid function. Monitoring of treatment is important.
- Author
- Xoct Yoct
- Language
- EN