Can I read Arrhythmogenic Right Ventricular Cardiomyopathy: a Focused Update on Diagnosis and Risk Stratification on EtoBox?

Arrhythmogenic Right Ventricular Cardiomyopathy: a Focused Update on Diagnosis and Risk Stratification by Laurens P Bosman; Anneline S J M te Riele is a Medicine article available to read on EtoBox.

What is Arrhythmogenic Right Ventricular Cardiomyopathy: a Focused Update on Diagnosis and Risk Stratification about?

Arrhythmogenic right ventricular cardiomyopathy (ARVC) is an inherited cardiomyopathy characterised by fibrofatty replacement of predominantly the right ventricle and high risk of ventricular arrhythmias and sudden cardiac death (SCD). Early diagnosis and accurate risk assessment are challenging yet essential for SCD prevention. This manuscript summarises the current state of the art on ARVC diagnosis and risk stratification. Improving the 2010 diagnostic criteria is an ongoing discussion. Several studies suggest that early diagnosis may be facilitated by including deformation imaging (‘strain’) for objective assessment of wall motion abnormalities, which was shown to have high sensitivity for preclinical disease. Adding fibrofatty replacement detected by late gadolinium enhancement or T1 mapping in cardiac MRI as criterion for diagnosis is increasingly suggested but requires more supporting evidence from consecutive patient cohorts. In addition to the traditional right-dominant ARVC, standard criteria for arrhythmogenic cardiomyopathy (ACM) and arrhythmogenic left ventricular cardiomyopathy (ALVC) are on the horizon. After diagnosis confirmation, the primary management goal is SCD

Who reads Arrhythmogenic Right Ventricular Cardiomyopathy: a Focused Update on Diagnosis and Risk Stratification?

Author

Laurens P Bosman; Anneline S J M te Riele

Publisher

BMJ

Published

2021

Language

EN

Field

Medicine (Health Sciences)