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Ependymoma Presenting as a ­Rim-Enhancing Lesion in the Brainstem by Fatema Malbari; Guillermo Aldave; Sherri B. Birchansky; Arnold C. Paulino; Dolores H. Lopez-Terrada; Carrie A. Mohila; Sibo Zhao; Murali Chintagumpala is a Medicine article available to read on EtoBox.

What is Ependymoma Presenting as a ­Rim-Enhancing Lesion in the Brainstem about?

**__Introduction:__** The posterior fossa is the most common intracranial location for pediatric ependymoma. While ependymoma usually arises from the ventricular lining of the fourth ventricle as a solid mass, it rarely originates from the brainstem. Grade II ependymomas also infrequently appear as a cavitary ring-enhancing lesion. **__Case Presentation:__** We describe a case of a 6-year-old boy with an ependymoma arising within the medulla with imaging features of a thick-walled rim-enhancing cavitary lesion. A stereotactic biopsy was obtained which confirmed a grade II ependymoma. The patient received focal proton beam radiation therapy and is doing well with no concerns for disease progression at 28 months after diagnosis. **__Conclusion:__** Posterior fossa ependymomas typically arise from ependymal cells within the fourth ventricle or foramina of Luschka. They rarely invade or arise within the brainstem parenchyma. Our case had atypical imaging findings in addition to the atypical tumor location. The lesion was described as a thick-walled rim-enhancing focal cystic necrotic lesion centered within the medulla with surrounding nonenhancing expansile infiltrative changes. Ring-e

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Author

Fatema Malbari; Guillermo Aldave; Sherri B. Birchansky; Arnold C. Paulino; Dolores H. Lopez-Terrada; Carrie A. Mohila; Sibo Zhao; Murali Chintagumpala

Publisher

S. Karger AG

Published

2021

Language

EN

Field

Medicine (Health Sciences)