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Rare Case of Severe Non-calcific Aortic Stenosis in an Achondroplastic Dwarf: Surgical Consideration by Tsubasa Mikami; Satoshi Kainuma; Koichi Toda; Yoshiki Sawa is a Medicine article available to read on EtoBox.

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## Abstract A 41-year-old patient with achondroplasia who had undergone surgery for congenital aortic stenosis >20 years ago presented with dyspnoea due to severe aortic stenosis. Computed tomography confirmed a small (16-mm) aortic annulus, thickened aortic valve leaflets without calcification and subaortic fibrous tissues. Intraoperatively, 3 non-calcific aortic leaflets were observed. Enlargement of the aortic root using a modified Manouguian technique for good exposure enabled the resection of subaortic tissues and replacement of the valve with a mechanical valve. The aortic root can be extremely small in patients with aortic stenosis and achondroplasia. The anatomy of the aortic root should be carefully assessed to enable appropriate surgical planning.

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Author

Tsubasa Mikami; Satoshi Kainuma; Koichi Toda; Yoshiki Sawa

Publisher

Oxford University Press (OUP)

Published

2021

Language

EN

Field

Medicine (Health Sciences)